Opsoclonus-myoclonus syndrome (Kinsbourne’s syndrome)
V. M. Alifirova,
T. A. Valikova,
N. V. Pugachenko,
N. V. Kubar,
M. N. Azhermacheva,
N. B. Vershinina,
S. D. Kazakov,
E. S. Koroleva https://doi.org/10.20538/1682-0363-2019-4-233-238
Abstract
Kinsbourne’s syndrome or opsoklonus-myoclonus syndrome is an autoimmune disease of the central nervous system mainly affecting the cerebellum and its connections. The disease is characterized by progressive course and is rarely observed. There is no accurate data on the prevalence of opsoklonusmyoclonus syndrome in Russia. The etiology and pathogenesis of the disease are being studied. This disease can develop against the background of cancer, infectious diseases and vaccinations. The article presents a ñlinical case of this rare pathology.
About the Authors
V. M. Alifirova
Siberian State Medical University (SSMU)
Russian Federation
Russian Federation
DM, Professor, Head of the Department of Neurology and Neurosurgery,
2, Moscow Trakt, Tomsk, 634050
T. A. Valikova
Siberian State Medical University (SSMU)
Russian Federation
Russian Federation
PhD, Associate Professor, Department of Neurology and Neurosurgery,
2, Moscow Trakt, Tomsk, 634050
N. V. Pugachenko
Siberian State Medical University (SSMU)
Russian Federation
Russian Federation
PhD, Associate Professor, Department of Neurology and Neurosurgery,
2, Moscow Trakt, Tomsk, 634050
N. V. Kubar
Tomsk Regional Clinical Hospital
Russian Federation
Russian Federation
Nevrologist, Department of Neurology,
96, Ivana Chernykh Str., Tomsk, 634063
M. N. Azhermacheva
Siberian State Medical University (SSMU)
Russian Federation
Russian Federation
PhD, Associate Professor, Department of Neurology and Neurosurgery,
2, Moscow Trakt, Tomsk, 634050
N. B. Vershinina
Tomsk Regional Clinical Hospital
Russian Federation
Russian Federation
Nevrologist, Chief of the Department of Neurology,
96, Ivana Chernykh Str., Tomsk, 634063
S. D. Kazakov
Siberian State Medical University (SSMU)
Russian Federation
Russian Federation
Post-Graduate Student, Department of Neurology and Neurosurgery,
2, Moscow Trakt, Tomsk, 634050
E. S. Koroleva
Siberian State Medical University (SSMU)
Russian Federation
Russian Federation
PhD, Associate Professor, Department of Neurology and Neurosurgery,
2, Moscow Trakt, Tomsk, 634050
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Review
For citations:
Alifirova V.M., Valikova T.A., Pugachenko N.V., Kubar N.V., Azhermacheva M.N., Vershinina N.B., Kazakov S.D., Koroleva E.S. Opsoclonus-myoclonus syndrome (Kinsbourne’s syndrome). Bulletin of Siberian Medicine. 2019;18(4):233-238. (In Russ.) https://doi.org/10.20538/1682-0363-2019-4-233-238
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