Pulmonary histocytosis X: clinical observation of early-stage disease
https://doi.org/10.20538/1682-0363-2017-2-195-201
Abstract
Histocytosis X is a rare disease of unknown etiology involving the reticuloendothelial system. We present a case of a 32 year-old man diagnosed with Pulmonary Histocytisis X. The CT image of the lungs showed disseminated disease with the formation of cyst-like cavities, which were histologically verified using lung biopsy.
About the Authors
Irina G. Frolova
Tomsk Cancer Research Institute, Tomsk National Research Medical Center (TNRMC), Russian Academy of Sciences (RAS)
Russian Federation
Russian Federation
DM, Professor, Head of the Diagnostic Imaging Department
12/а, Savinuh Str., 634028, Tomsk
Svetlana A. Velichko
Tomsk Cancer Research Institute, Tomsk National Research Medical Center (TNRMC), Russian Academy of Sciences (RAS)
Russian Federation
Russian Federation
DM, Professor, Principal Investigator, Imaging Department
12/а, Savinuh Str., 634028, Tomsk
Aleksey V. Goldberg
Tomsk Cancer Research Institute, Tomsk National Research Medical Center (TNRMC), Russian Academy of Sciences (RAS)
Russian Federation
Russian Federation
Junior Researcher, Diagnostic Imaging Department
12/а, Savinuh Str., 634028, Tomsk
Sergey A. Tuzikov
Tomsk Cancer Research Institute, Tomsk National Research Medical Center (TNRMC), Russian Academy of Sciences (RAS)
Russian Federation
Russian Federation
DM, Professor, Head of Thoracic and Abdominal Department
12/а, Savinuh Str., 634028, Tomsk
Sergey A. Miller
Tomsk Cancer Research Institute, Tomsk National Research Medical Center (TNRMC), Russian Academy of Sciences (RAS)
Russian Federation
Russian Federation
DM, Leading Researcher, Thoracic and Abdominal Department
12/а, Savinuh Str., 634028, Tomsk
Evgeniy O. Rodionov
Tomsk Cancer Research Institute, Tomsk National Research Medical Center (TNRMC), Russian Academy of Sciences (RAS)
Russian Federation
Russian Federation
Postgraduate Student, Thoracic and Abdominal Department
12/а, Savinuh Str., 634028, Tomsk
Leonid A. Efteev
Tomsk Cancer Research Institute, Tomsk National Research Medical Center (TNRMC), Russian Academy of Sciences (RAS)
Russian Federation
Russian Federation
Junior Researcher, Thoracic and Abdominal Department
12/а, Savinuh Str., 634028, Tomsk
Ludmila N. Bondar
Tomsk Cancer Research Institute, Tomsk National Research Medical Center (TNRMC), Russian Academy of Sciences (RAS)
Russian Federation
Russian Federation
PhD, Doctor, Department of Pathological Anatomy and Cytology
12/а, Savinuh Str., 634028, Tomsk
Vladimir M. Perelmuter
Tomsk Cancer Research Institute, Tomsk National Research Medical Center (TNRMC), Russian Academy of Sciences (RAS)
Russian Federation
Russian Federation
DM, Professor, Head of Department of Pathological Anatomy and Cytology
12/а, Savinuh Str., 634028, Tomsk
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Review
For citations:
Frolova I.G., Velichko S.A., Goldberg A.V., Tuzikov S.A., Miller S.A., Rodionov E.O., Efteev L.A., Bondar L.N., Perelmuter V.M. Pulmonary histocytosis X: clinical observation of early-stage disease. Bulletin of Siberian Medicine. 2017;16(2):195-201. (In Russ.) https://doi.org/10.20538/1682-0363-2017-2-195-201
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